Patient-reported outcomes in patients with acromegaly treated with pegvisomant in the ACROSTUDY extension: A real-world experience


Por: Salvatori, R, Maffei, P, Webb, SM, Brue, T, Loftus, J, Valluri, SR, Gomez, R, Wajnrajch, MP, Fleseriu, M

Publicada: 1 jun 2022 Ahead of Print: 1 ene 2022
Resumen:
Purpose To report the effects of pegvisomant (PEGV) treatment on patient-reported outcomes in acromegaly patients. Methods We conducted an extension study of an open-label, multinational, non-interventional study (ACROSTUDY) evaluating the long-term safety and efficacy of PEGV for acromegaly in routine clinical practice. Enrolled patients were rollover patients from ACROSTUDY, or treatment naive/semi-naive (NSN; no PEGV within 6 months of enrollment). Exploratory efficacy endpoints were changes in symptoms with the Patient-Assessed Acromegaly Symptom Questionnaire (PASQ) and quality of life with the Acromegaly Quality of Life questionnaire (AcroQoL) analyzed by controlled or uncontrolled IGF-I levels. Results were analyzed in all patients, in NSN patient subgroup, and by diabetes status. Results A total of 544 patients with acromegaly were enrolled, including 434 rollover subjects from ACROSTUDY and 110 NSN patients. Mean PEGV treatment duration was 7.8 years (range, 0-19.6 years). Overall, the majority of PASQ scores improved over time, but there was no significant difference between IGF-I controlled or uncontrolled groups. In the NSN subgroup, most PASQ and AcroQoL scores remained similar to baseline up to 1 year, regardless of IGF-I control. Patients with diabetes reported better PASQ scores over time with PEGV treatment, regardless of IGF-I control. IGF-I normalization increased from 10% of patients at baseline to more than 78% at year 10, with a mean daily PEGV dose of 18.7 mg. Conclusions Overall, patients treated with PEGV had small improvements in PASQ. While IGF-I normalization increased with PEGV treatment, IGF-I control had no effects on PASQ and AcroQoL scores.

Filiaciones:
Salvatori, R:
 Johns Hopkins Univ, Div Endocrinol & Metab & Pituitary Ctr, Sch Med, Baltimore, MD 21218 USA

Maffei, P:
 Univ Padua, Dept Med DIMED, Padua, Italy

Webb, SM:
 Univ Autonoma Barcelona, Ctr Invest Biomed Red Enfermedades Raras, Dept Endocrinol Med, Hosp St Pau, Carrer St Quinti 89, Barcelona 08041, Spain

Brue, T:
 Hop Conception, Marseille, France

 Aix Marseille Univ, AP HM, Marseille Med Genet, Marseille, France

Loftus, J:
 Pfizer Ltd, Tadworth, England

Valluri, SR:
 Pfizer Inc, New York, NY USA

Gomez, R:
 Pfizer Inc, Brussels, Belgium

Wajnrajch, MP:
 Pfizer Inc, New York, NY USA

 NYU, Grossman Sch Med, Div Pediat Endocrinol, New York, NY USA

Fleseriu, M:
 Oregon Hlth & Sci Univ, Pituitary Ctr, Dept Med, Div Endocrinol Diabet & Clin Nutr & Neurol Surg, Portland, OR USA
ISSN: 1386341X
Editorial
SPRINGER, ONE NEW YORK PLAZA, SUITE 4600, NEW YORK, NY, UNITED STATES, USA
Tipo de documento: Article
Volumen: 25 Número: 3
Páginas: 420-432
WOS Id: 000741890400001
ID de PubMed: 35022929
imagen All Open Access; Green

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