Coronary computed tomographic angiography findings and their therapeutic implications in asymptomatic patients with familial hypercholesterolemia. Lessons from the SAFEHEART study


Por: de Isla, LP, Alonso, R, Muniz-Grijalvo, O, Diaz-Diaz, JL, Zambon, D, Miramontes, JP, Fuentes, F, de Diego, JJG, Gonzalez-Estrada, A, Mata, N, Saltijeral, A, Barreiro, M, Tomas, M, de Andres, R, Argues, R, Gotarredona, MPS, Herrero, SN, Palazon, RJP, de Caralt, TM, de Centi, LAS, Zhilina, S, Perez, SE, Padro, T, Mata, P

Publicada: 1 ago 2018
Resumen:
BACKGROUND: Familial hypercholesterolemia (FH) confers an increased risk of premature atherosclerotic disease. Coronary computed tomographic angiography (CTA) can assess preclinical coronary atherosclerosis. OBJECTIVES: To describe coronary CTA findings in asymptomatic molecularly defined FH individuals, to identify those factors related to its presence and extension, and to assess the impact of these results in patients' care and estimated risk. METHODS: Four hundred and forty individuals with FH, without clinical cardiovascular disease, were consecutively enrolled and underwent a coronary CTA that was used to analyze coronary atherosclerosis based on coronary calcium score (CCS), sum of stenosis severity, and plaque composition sum (PCS). For FH patients, cardiovascular risk was estimated using the specific SAFEHEART risk equation. Follow-up was performed using a standardized protocol. RESULTS: Mean age was 46.4 years (231 women, 52%). Coronary calcium was present in 55%, mean CCS was 130.9, 46% had a plaque with lumen involvement, and mean PCS was 1.1. During follow-up, there were 17 (4%) nonfatal events and 2 (1%) fatal events. CCS was independently associated to the estimated risk and low-density lipoprotein-cholesterol life-years, sum of stenosis severity to the estimated risk, and PCS to the estimated risk and low-density lipoprotein-cholesterol life-years. CTA findings induced a positive change in patients' care and in their estimated risk. CONCLUSION: Coronary artery atherosclerosis is highly prevalent in asymptomatic patients with FH and it is independently associated to cardiovascular risk. More advanced disease on CTA was associated with subsequent intensification of therapy and reduction of estimated risk. Further longitudinal studies are required to know if these findings might improve the risk stratification in patients with FH. (C) 2018 National Lipid Association. All rights reserved.

Filiaciones:
de Isla, LP:
 Univ Complutense, Hosp Clin San Carlos, Cardiol Dept, IDISSC, Madrid, Spain

 Fdn Hipercolesterolemia Familiar, C Gen Alvarez de Castro 14, Madrid, Spain

Alonso, R:
 Fdn Hipercolesterolemia Familiar, C Gen Alvarez de Castro 14, Madrid, Spain

 Clin Las Condes, Nutr Dept, Santiago, Chile

Muniz-Grijalvo, O:
 Hosp Virgen Rocio, UCERV UCAMI, Seville, Spain

Diaz-Diaz, JL:
 Hosp Abente & Lago, Dept Internal Med, La Coruna, Spain

Zambon, D:
 Univ Barcelona, IDIBAPS Inst Invest Biomed August Pi & Sunyer, Dept Endocrinol, Lipids Clin,Hosp Clin, Barcelona, Spain

Miramontes, JP:
 Hosp Univ Salamanca, Dept Internal Med, IBSAL, Salamanca, Spain

Fuentes, F:
 Univ Cordoba, IMIBIC Reina Sofia Univ Hosp, Lipids & Atherosclerosis Unit, Cordoba, Spain

de Diego, JJG:
 Fdn Hipercolesterolemia Familiar, C Gen Alvarez de Castro 14, Madrid, Spain

Gonzalez-Estrada, A:
 Hosp Virgen Rocio, UCERV UCAMI, Seville, Spain

Mata, N:
 Fdn Hipercolesterolemia Familiar, C Gen Alvarez de Castro 14, Madrid, Spain

 Madrid Hlth Author, Dept Epidemiol, Madrid, Spain

Saltijeral, A:
 Univ Alfonso X el Sabio, Hosp Tajo, Cardiol Dept, Madrid, Spain

Barreiro, M:
 Hosp Univ Salamanca, Cardiol Dept, Salamanca, Spain

Tomas, M:
 Fdn Jimenez Diaz, Radiol Dept, Madrid, Spain

de Andres, R:
 Fdn Jimenez Diaz, Internal Med Dept, Madrid, Spain

Argues, R:
 Hosp Univ Lugo, Endocrinol Dept, Lugo, Spain

Gotarredona, MPS:
 Hosp Virgen Rocio, Thorax Radiol Dept, Seville, Spain

Herrero, SN:
 Hosp Virgen Rocio, Thorax Radiol Dept, Seville, Spain

Palazon, RJP:
 Univ Barcelona, Inst Invest Biomed August Pi i Sunyer IDIBAPS, Hosp Clin Barcelona, Cardiothorac Radiol Dept,CDIC, Barcelona, Spain

de Caralt, TM:
 Univ Barcelona, Inst Invest Biomed August Pi i Sunyer IDIBAPS, Hosp Clin Barcelona, Cardiothorac Radiol Dept,CDIC, Barcelona, Spain

de Centi, LAS:
 Complejo Hosp Univ A Coruna, Radiol Dept, La Coruna, Spain

Zhilina, S:
 Hosp Univ Salamanca, Dept Internal Med, IBSAL, Salamanca, Spain

Perez, SE:
 Hosp Univ Reina Sofia, UGC Radiodiagnost, Cordoba, Spain

Padro, T:
 IIB St Pau, Inst Catalan Ciencias Cardiovasc, Barcelona, Spain
ISSN: 19332874





Journal of Clinical Lipidology
Editorial
ELSEVIER SCIENCE INC, STE 800, 230 PARK AVE, NEW YORK, NY 10169 USA, Estados Unidos America
Tipo de documento: Article
Volumen: 12 Número: 4
Páginas: 948-957
WOS Id: 000442192700017
ID de PubMed: 29753733

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