The poor prognosis of low hypodiploidy in adults with B-cell precursor acute lymphoblastic leukaemia is restricted to older adults and elderly patients


Por: Ribera, J, Granada, I, Morgades, M, Vives, S, Genesca, E, Gonzalez, C, Nomdedeu, J, Escoda, L, Montesinos, P, Mercadal, S, Coll, R, Gonzalez-Campos, J, Abella, E, Barba, P, Bermudez, A, Gil, C, Tormo, M, Pedreno, M, Martinez-Carballeira, D, Hernandez-Rivas, JM, Orfao, A, Martinez-Lopez, J, Esteve, J, Bravo, P, Garcia-Guinon, A, Deben, G, Moraleda, JM, Queizan, JA, Ortin, X, Moreno, MJ, Feliu, E, Sole, F, Ribera, JM

Publicada: 1 jul 2019
Resumen:
The prognostic significance of low-hypodiploidy has not been extensively evaluated in minimal residual disease (MRD)-oriented protocols for adult acute lymphoblastic leukaemia (ALL). We analysed the outcome of hypodiploid adult ALL patients treated within Programa Espanol de Tratamientos en Hematologia (PETHEMA) protocols. The 5-year cumulative incidence of relapse (CIR) of low-hypodiploid B-cell precursor (BCP)-ALL was significantly higher than that of high-hypodiploids (52% vs. 12%, P = 0.013). Low-hypodiploid BCP-ALL patients aged <= 35 years showed superior survival (71% vs. 21%, P = 0.026) and lower 5-year CIR (17% vs. 66%, P = 0.090) than low-hypodiploids aged >35 years. Older adults and elderly low-hypodiploid BCP-ALL patients show dismal prognosis although achieving an end-induction good MRD response.

Filiaciones:
Ribera, J:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

 Hosp Badalona Germans Trias & Pujol, Inst Catala Oncol, Barcelona, Spain

Granada, I:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

 Hosp Badalona Germans Trias & Pujol, Inst Catala Oncol, Barcelona, Spain

Morgades, M:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

 Hosp Badalona Germans Trias & Pujol, Inst Catala Oncol, Barcelona, Spain

Vives, S:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

 Hosp Badalona Germans Trias & Pujol, Inst Catala Oncol, Barcelona, Spain

Genesca, E:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

Gonzalez, C:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

Nomdedeu, J:
 Hosp Santa Creu & Sant Pau, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

Escoda, L:
 Hosp Joan 23, Inst Catala Oncol, Tarragona, Spain

Montesinos, P:
 Hosp La Fe, Valencia, Spain

Mercadal, S:
 Hospitalet Llobregat, Hosp Duran & Reynals, Inst Catala Oncol, Lhospitalet De Llobregat, Spain

Coll, R:
 Hosp Josep Trueta, Inst Catala Oncol, Girona, Spain

Gonzalez-Campos, J:
 Hosp Univ Virgen Rocio, Seville, Spain

Abella, E:
 Hosp Mar, Barcelona, Spain

Barba, P:
 Hosp Valle De Hebron, Barcelona, Spain

Bermudez, A:
 Hosp Marques Valdecilla, Santander, Spain

Gil, C:
 Hosp Gen Alicante, Alicante, Spain

Tormo, M:
 Hosp Clin, Valencia, Spain

Pedreno, M:
 Hosp Doctor Peset, Valencia, Spain

Martinez-Carballeira, D:
 Hosp Univ Cent Asturias, Oviedo, Spain

Hernandez-Rivas, JM:
 Univ Salamanca, Hosp Univ Salamanca, IBMCC CSIC USAL, IBSAL, Salamanca, Spain

 CIBERONC, Salamanca, Spain

 Hosp Doce Octubre, Madrid, Spain

Orfao, A:
 Univ Salamanca, Hosp Univ Salamanca, IBMCC CSIC USAL, IBSAL, Salamanca, Spain

 CIBERONC, Salamanca, Spain

Martinez-Lopez, J:
 Hosp Doce Octubre, Madrid, Spain

Esteve, J:
 Hosp Clin Barcelona, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

Bravo, P:
 Hosp Univ Fuenlabrada Fuenlabrada, Lleida, Spain

Garcia-Guinon, A:
 Hosp Arnau Vilanova, Lleida, Spain

Deben, G:
 Hosp Juan Canalejo, La Coruna, Spain

Moraleda, JM:
 Univ Murcia, Hosp Clin Univ Virgen Arrixaca, IMIB, Murcia, Spain

Queizan, JA:
 Hosp Gen Segovia, Segovia, Spain

Ortin, X:
 Hosp Verge Cinta, Tortosa, Spain

Moreno, MJ:
 Hosp Virgen Victoria, Malaga, Spain

Feliu, E:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

 Hosp Badalona Germans Trias & Pujol, Inst Catala Oncol, Barcelona, Spain

Sole, F:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

Ribera, JM:
 Univ Autonoma Barcelona, Hosp Germans Trias & Pujol, Inst Recerca Leucemia Josep Carreras, Barcelona, Spain

 Hosp Badalona Germans Trias & Pujol, Inst Catala Oncol, Barcelona, Spain
ISSN: 00071048





BRITISH JOURNAL OF HAEMATOLOGY
Editorial
WILEY, 111 RIVER ST, HOBOKEN 07030-5774, NJ USA, GB
Tipo de documento: Article
Volumen: 186 Número: 2
Páginas: 263-268
WOS Id: 000474639800009
ID de PubMed: 30916384
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