ApoB100 remodeling and stiffened cholesteryl ester core raise LDL aggregation in familial hypercholesterolemia patients


Por: Lhoëst, MTL, Martínez, A, Garcia, E, Dandurand, J, Polishchuk, A, Benitez-Amaro, A, Cenarro, A, Civeira, F, Bernabé, A, Vilades, D, Escolà-Gil, JC, Samouillan, V, Llorente-Cortes, V

Publicada: 1 ene 2025 Ahead of Print: 1 dic 2024
Resumen:
Patients with familial hypercholesterolemia (FH) exhibit a significant residual cardiovascular risk. A new cardiovascular risk factor is the susceptibility of individual LDL particles to aggregation. This study examined LDL aggregation and its relationship with LDL lipid composition and biophysical properties in patients with FH compared to controls. LDL aggregation was measured as the change in particle size, assessed by dynamic light scattering, after exposure to sphingomyelinase, which breaks down sphingomyelin in the LDL phospholipid layer. Dynamic light scattering and transmission electron microscopy showed that LDL in FH patients exhibited smaller size and greater susceptibility to aggregation. Biochemical analyses revealed a higher cholesteryl ester (CE)/ApoB100 ratio in LDL from FH patients. Differential scanning calorimetry showed that LDL from FH patients had higher transition temperatures, indicating a more ordered CE core. Fourier transform infrared spectroscopy revealed fewer flexible alpha-helices (1658 cm- 1 ) and more stable alpha-helices (1651 cm- 1 ) in ApoB100 of LDL from FH patients. These structural changes correlated with higher CE content and increased LDL aggregation. In conclusion, a more ordered CE core in smaller LDL particles, combined with a higher proportion of stable alpha-helices in ApoB100, promotes LDL aggregation in FH patients. These findings suggest ApoB100 conformational structure as a new potential therapeutic targets within LDL to reduce cardiovascular risk in FH patients.

Filiaciones:
Lhoëst, MTL:
 CSIC, Inst Biomed Res Barcelona IIBB, Expt Pathol Dept, Barcelona, Spain

 Biomed Res Inst St Pau IIB St Pau, Cardiovasc Area, Barcelona, Spain

 Inst Invest Biomed IIB St Pau, Inst Recerca Hosp St Creu i St Pau, Cardiovasc Area, Barcelona, Spain

 Univ Autonoma Barcelona, Biochem Dept, Barcelona, Spain

Martínez, A:
 CSIC, Inst Biomed Res Barcelona IIBB, Expt Pathol Dept, Barcelona, Spain

 Biomed Res Inst St Pau IIB St Pau, Cardiovasc Area, Barcelona, Spain

 Inst Invest Biomed IIB St Pau, Inst Recerca Hosp St Creu i St Pau, Cardiovasc Area, Barcelona, Spain

Garcia, E:
 CSIC, Inst Biomed Res Barcelona IIBB, Expt Pathol Dept, Barcelona, Spain

 Biomed Res Inst St Pau IIB St Pau, Cardiovasc Area, Barcelona, Spain

 Inst Invest Biomed IIB St Pau, Inst Recerca Hosp St Creu i St Pau, Cardiovasc Area, Barcelona, Spain

 Univ Autonoma Barcelona, Biochem Dept, Barcelona, Spain

Dandurand, J:
 Univ Toulouse Paul Sabatier, Equipe PHYPOL, CIRIMAT, Toulouse, France

Polishchuk, A:
 CSIC, Inst Biomed Res Barcelona IIBB, Expt Pathol Dept, Barcelona, Spain

 Biomed Res Inst St Pau IIB St Pau, Cardiovasc Area, Barcelona, Spain

 Inst Invest Biomed IIB St Pau, Inst Recerca Hosp St Creu i St Pau, Cardiovasc Area, Barcelona, Spain

Benitez-Amaro, A:
 CSIC, Inst Biomed Res Barcelona IIBB, Expt Pathol Dept, Barcelona, Spain

 Biomed Res Inst St Pau IIB St Pau, Cardiovasc Area, Barcelona, Spain

 Inst Invest Biomed IIB St Pau, Inst Recerca Hosp St Creu i St Pau, Cardiovasc Area, Barcelona, Spain

Cenarro, A:
 Univ Zaragoza, Hosp Univ Miguel Servet, IIS Aragon, Inst Aragones Ciencias Salud, Zaragoza, Spain

 Inst Hlth Carlos III, CIBER Enfermedades Cardiovasc CIBERCV, Madrid, Spain

Civeira, F:
 Univ Zaragoza, Hosp Univ Miguel Servet, IIS Aragon, Inst Aragones Ciencias Salud, Zaragoza, Spain

 Inst Hlth Carlos III, CIBER Enfermedades Cardiovasc CIBERCV, Madrid, Spain

Bernabé, A:
 CSIC, Inst Ciencia Mat Barcelona ICMAB, Campus UAB, Bellaterra, Spain

Vilades, D:
 IIB ST PAU, Hosp Santa Creu i St Pau, Dept Cardiol, Cardiac Imaging Unit, Barcelona, Spain

Escolà-Gil, JC:
 Inst Invest Biomed IIB St Pau, Inst Recerca Hosp St Creu i St Pau, Cardiovasc Area, Barcelona, Spain

 Univ Autonoma Barcelona, Biochem Dept, Barcelona, Spain

 CIBER Diabet & Enfermedades Metab Asociadas CIBERD, Madrid, Spain

Samouillan, V:
 Univ Toulouse Paul Sabatier, Equipe PHYPOL, CIRIMAT, Toulouse, France

Llorente-Cortes, V:
 CSIC, Inst Biomed Res Barcelona IIBB, Expt Pathol Dept, Barcelona, Spain

 Biomed Res Inst St Pau IIB St Pau, Cardiovasc Area, Barcelona, Spain

 Inst Invest Biomed IIB St Pau, Inst Recerca Hosp St Creu i St Pau, Cardiovasc Area, Barcelona, Spain

 Inst Hlth Carlos III, CIBER Enfermedades Cardiovasc CIBERCV, Madrid, Spain
ISSN: 00222275





JOURNAL OF LIPID RESEARCH
Editorial
AMER SOC BIOCHEMISTRY MOLECULAR BIOLOGY INC, 9650 ROCKVILLE PIKE, BETHESDA, MD 20814-3996 USA, Estados Unidos America
Tipo de documento: Article
Volumen: 66 Número: 1
Páginas:
WOS Id: 001395928200001
ID de PubMed: 39557294
imagen Green Submitted, Green Accepted, gold

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