Crossed-reflex in antiphospholipid chorea
Por:
Fernández-Vidal, JM, Olmedo-Saura, G, Querol-Gutiérrez, LA, Kulisevsky, J, Pérez-Pérez, J
Publicada:
19 jun 2024
Ahead of Print:
1 jun 2024
Resumen:
Chorea is a hyperkinetic movement disorder associated with various underlyingconditions, including autoimmune diseases such as antiphospholipid syndrome (APS). APS can manifest with a wide range of neurological symptoms, including chorea. We present a case of a 77-year-old man with subacute generalized chorea secondary to primary APS. Notably, the patient exhibited a left patellar crossed-reflex, a phenomenon rarely documented in chorea cases, the pathophysiology of which has not yet been elucidated. In summary, this case challenges the traditional demographics of antiphospholipid syndrome (APS) by suggesting a potential link between APS and late-age patients. It emphasizes the importance of considering APS in late-onset chorea cases.
Filiaciones:
Fernández-Vidal, JM:
Hosp Santa Creu & Sant Pau, Dept Neurol, Barcelona, Spain
Olmedo-Saura, G:
Hosp Santa Creu & Sant Pau, Dept Neurol, Barcelona, Spain
Hosp Santa Creu & Sant Pau, Dept Neurol, Movement Disorders Unit, 90 Mas Casanovas St, Barcelona 08040, Spain
Network Res Ctr Neurodegenerat Dis CIBERNED, Madrid, Spain
Barcelona Autonomous Univ, Dept Med, Barcelona, Spain
Querol-Gutiérrez, LA:
Hosp Santa Creu & Sant Pau, Dept Neurol, Barcelona, Spain
Hosp Santa Creu & Sant Pau, Dept Neurol, Neuromuscular Dis Unit, Barcelona, Spain
Network Res Ctr Rare Dis CIBERER, Madrid, Spain
Barcelona Autonomous Univ, Dept Med, Barcelona, Spain
Kulisevsky, J:
Hosp Santa Creu & Sant Pau, Dept Neurol, Barcelona, Spain
Hosp Santa Creu & Sant Pau, Dept Neurol, Movement Disorders Unit, 90 Mas Casanovas St, Barcelona 08040, Spain
Network Res Ctr Neurodegenerat Dis CIBERNED, Madrid, Spain
Barcelona Autonomous Univ, Dept Med, Barcelona, Spain
Pérez-Pérez, J:
Hosp Santa Creu & Sant Pau, Dept Neurol, Barcelona, Spain
Hosp Santa Creu & Sant Pau, Dept Neurol, Movement Disorders Unit, 90 Mas Casanovas St, Barcelona 08040, Spain
Network Res Ctr Neurodegenerat Dis CIBERNED, Madrid, Spain
Barcelona Autonomous Univ, Dept Med, Barcelona, Spain
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