State of the art of Mohs surgery for rare cutaneous tumors in the Spanish Registry of Mohs Surgery (REGESMOHS)


Por: Rodriguez-Jimenez, P, Jimenez, YD, Reolid, A, Sanmartin-Jimenez, O, Garces, JR, Rodriguez-Prieto, MA, Medrano, RM, Vilarrasa, E, de Eusebio-Murillo, E, Redondo, P, Ciudad-Blanco, C, Morales-Gordillo, V, Toll-Abello, A, Artola-Igarza, JL, Pacheco, MLA, Markixana, IA, Fernandez, RS, Rubio, AA, Vazquez-Veiga, H, Florez-Menendez, A, Dobao, PD, Botella-Estrada, R, Garcia-Bracamonte, B, Carnero-Gonzalez, L, Ruiz-Salas, V, Sanchez-Sambucety, P, Lopez-Estebaranz, JL, Gil, P, Barchino, L, Arenal, MM, Ocerin-Guerra, I, Hueso, L, Seoane-Pose, MJ, Gonzalez-Sixto, B, Cano-Martinez, N, Escutia-Munoz, B, Ortiz-Romero, PL, Garcia-Doval, I, Descalzo, MA

Publicada: 1 mar 2020 Ahead of Print: 1 nov 2019
Resumen:
Background The use of Mohs micrographic surgery (MMS) for rare cutaneous tumors is poorly defined. We aim to describe the demographics, tumor presentation and topography, surgery characteristics and complications of MMS for rare cutaneous tumors in a national registry. Methods Prospective cohort study of patients treated with MMS in Spain between July 2013 and June 2018. The inclusion criteria were patients with cutaneous tumors with final diagnosis different from basal cell carcinoma, squamous cell carcinoma, dermatofibrosarcoma protuberans, or any kind of melanoma. Results Five thousand and ninety patients were recorded in the registry, from which only 73 tumors (1.4%) fulfilled the inclusion criteria: atypical fibroxanthoma (18), microcystic adnexal carcinoma (10), extramammary Paget's disease (7), Merkel cell carcinoma (5), dermatofibroma (4), trichilemmal carcinoma (4), desmoplastic trichoepithelioma (4), sebaceous carcinoma (3), leiomyosarcoma (2), porocarcinoma (2), angiosarcoma (2), trichoblastoma (1), superficial acral fibromyxoma (1), and others (10). No intra-surgery morbidity was registered. Postsurgery complications appeared in six patients (9%) and were considered mild. Median follow-up time was 0.9 years during which three Merkel cell carcinomas, one angiosarcoma, one microcystic adnexal carcinoma, and four others recurred (12.3%). Conclusion This national registry shows that rare cutaneous tumors represent a negligible part of the total MMS performed in our country with a low complication rate.

Filiaciones:
Rodriguez-Jimenez, P:
 Hosp Univ Princesa, Madrid, Spain

Jimenez, YD:
 Hosp Univ Princesa, Madrid, Spain

 Hosp Univ Quiron Salud, Madrid, Spain

Reolid, A:
 Hosp Univ Princesa, Madrid, Spain

Sanmartin-Jimenez, O:
 Inst Valenciano Oncol, Valencia, Spain

Garces, JR:
 Hosp Santa Creu & Sant Pau, Barcelona, Spain

 Ctr Med Teknon, Barcelona, Spain

Rodriguez-Prieto, MA:
 Complejo Asistencial Univ Leon, Leon, Spain

Medrano, RM:
 Hosp Univ Fdn Alcorcon, Madrid, Spain

Vilarrasa, E:
 Hosp Santa Creu & Sant Pau, Barcelona, Spain

 Ctr Med Teknon, Barcelona, Spain

de Eusebio-Murillo, E:
 Complejo Hosp Univ Guadalajara, Guadalajara, Spain

Redondo, P:
 Clin Univ Navarra, Pamplona, Spain

Ciudad-Blanco, C:
 Hosp La Zarzuela, Madrid, Spain

 Hosp Gregorio Maranon, Madrid, Spain

Morales-Gordillo, V:
 Hosp Univ Quiron Salud, Madrid, Spain

Toll-Abello, A:
 Hosp del Mar, Barcelona, Spain

Artola-Igarza, JL:
 Hosp Galdakao, Galdakao, Spain

Pacheco, MLA:
 Hosp La Paz, Madrid, Spain

Markixana, IA:
 Hosp Univ Cruces, Baracaldo, Spain

Fernandez, RS:
 Hosp Gregorio Maranon, Madrid, Spain

Rubio, AA:
 Hosp Manises, Valencia, Spain

Vazquez-Veiga, H:
 Complexo Hosp Univ Santiago, Santiago de Compostela, Spain

Florez-Menendez, A:
 Complejo Univ Hosp Pontevedra, Pontevedra, Spain

Dobao, PD:
 Hosp Infanta Leonor, Madrid, Spain

Botella-Estrada, R:
 Hosp Univ La Fe, Valencia, Spain

Garcia-Bracamonte, B:
 Hosp Univ Doce Octubre, Madrid, Spain

Carnero-Gonzalez, L:
 Hosp Univ Araba, Vitoria, Spain

Ruiz-Salas, V:
 Hosp Santa Creu & Sant Pau, Barcelona, Spain

Sanchez-Sambucety, P:
 Complejo Asistencial Univ Leon, Leon, Spain

Lopez-Estebaranz, JL:
 Hosp Univ Fdn Alcorcon, Madrid, Spain

Gil, P:
 Clin Univ Navarra, Pamplona, Spain

Barchino, L:
 Hosp La Zarzuela, Madrid, Spain

Arenal, MM:
 Hosp La Paz, Madrid, Spain

Ocerin-Guerra, I:
 Hosp Univ Cruces, Baracaldo, Spain

Hueso, L:
 Hosp Manises, Valencia, Spain

Seoane-Pose, MJ:
 Complexo Hosp Univ Santiago, Santiago de Compostela, Spain

Gonzalez-Sixto, B:
 Complejo Univ Hosp Pontevedra, Pontevedra, Spain

Cano-Martinez, N:
 Hosp La Zarzuela, Madrid, Spain

 Hosp Infanta Leonor, Madrid, Spain

Escutia-Munoz, B:
 Hosp Univ La Fe, Valencia, Spain

Ortiz-Romero, PL:
 Hosp Univ Doce Octubre, Madrid, Spain

Garcia-Doval, I:
 Complexo Hosp Univ Vigo, Vigo, Spain

 Acad Espanola Dermatol, Fdn Piel Sana, Madrid, Spain

Descalzo, MA:
 Acad Espanola Dermatol, Fdn Piel Sana, Madrid, Spain
ISSN: 00119059





INTERNATIONAL JOURNAL OF DERMATOLOGY
Editorial
WILEY, 111 RIVER ST, HOBOKEN 07030-5774, NJ USA, Estados Unidos America
Tipo de documento: Article
Volumen: 59 Número: 3
Páginas: 321-325
WOS Id: 000499030100001
ID de PubMed: 31777957

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