State of the art of Mohs surgery for rare cutaneous tumors in the Spanish Registry of Mohs Surgery (REGESMOHS)
Por:
Rodriguez-Jimenez, P, Jimenez, YD, Reolid, A, Sanmartin-Jimenez, O, Garces, JR, Rodriguez-Prieto, MA, Medrano, RM, Vilarrasa, E, de Eusebio-Murillo, E, Redondo, P, Ciudad-Blanco, C, Morales-Gordillo, V, Toll-Abello, A, Artola-Igarza, JL, Pacheco, MLA, Markixana, IA, Fernandez, RS, Rubio, AA, Vazquez-Veiga, H, Florez-Menendez, A, Dobao, PD, Botella-Estrada, R, Garcia-Bracamonte, B, Carnero-Gonzalez, L, Ruiz-Salas, V, Sanchez-Sambucety, P, Lopez-Estebaranz, JL, Gil, P, Barchino, L, Arenal, MM, Ocerin-Guerra, I, Hueso, L, Seoane-Pose, MJ, Gonzalez-Sixto, B, Cano-Martinez, N, Escutia-Munoz, B, Ortiz-Romero, PL, Garcia-Doval, I, Descalzo, MA
Publicada:
1 mar 2020
Ahead of Print:
1 nov 2019
Resumen:
Background The use of Mohs micrographic surgery (MMS) for rare cutaneous tumors is poorly defined. We aim to describe the demographics, tumor presentation and topography, surgery characteristics and complications of MMS for rare cutaneous tumors in a national registry. Methods Prospective cohort study of patients treated with MMS in Spain between July 2013 and June 2018. The inclusion criteria were patients with cutaneous tumors with final diagnosis different from basal cell carcinoma, squamous cell carcinoma, dermatofibrosarcoma protuberans, or any kind of melanoma. Results Five thousand and ninety patients were recorded in the registry, from which only 73 tumors (1.4%) fulfilled the inclusion criteria: atypical fibroxanthoma (18), microcystic adnexal carcinoma (10), extramammary Paget's disease (7), Merkel cell carcinoma (5), dermatofibroma (4), trichilemmal carcinoma (4), desmoplastic trichoepithelioma (4), sebaceous carcinoma (3), leiomyosarcoma (2), porocarcinoma (2), angiosarcoma (2), trichoblastoma (1), superficial acral fibromyxoma (1), and others (10). No intra-surgery morbidity was registered. Postsurgery complications appeared in six patients (9%) and were considered mild. Median follow-up time was 0.9 years during which three Merkel cell carcinomas, one angiosarcoma, one microcystic adnexal carcinoma, and four others recurred (12.3%). Conclusion This national registry shows that rare cutaneous tumors represent a negligible part of the total MMS performed in our country with a low complication rate.
Filiaciones:
Rodriguez-Jimenez, P:
Hosp Univ Princesa, Madrid, Spain
Jimenez, YD:
Hosp Univ Princesa, Madrid, Spain
Hosp Univ Quiron Salud, Madrid, Spain
Reolid, A:
Hosp Univ Princesa, Madrid, Spain
Sanmartin-Jimenez, O:
Inst Valenciano Oncol, Valencia, Spain
Garces, JR:
Hosp Santa Creu & Sant Pau, Barcelona, Spain
Ctr Med Teknon, Barcelona, Spain
Rodriguez-Prieto, MA:
Complejo Asistencial Univ Leon, Leon, Spain
Medrano, RM:
Hosp Univ Fdn Alcorcon, Madrid, Spain
Vilarrasa, E:
Hosp Santa Creu & Sant Pau, Barcelona, Spain
Ctr Med Teknon, Barcelona, Spain
de Eusebio-Murillo, E:
Complejo Hosp Univ Guadalajara, Guadalajara, Spain
Redondo, P:
Clin Univ Navarra, Pamplona, Spain
Ciudad-Blanco, C:
Hosp La Zarzuela, Madrid, Spain
Hosp Gregorio Maranon, Madrid, Spain
Morales-Gordillo, V:
Hosp Univ Quiron Salud, Madrid, Spain
Toll-Abello, A:
Hosp del Mar, Barcelona, Spain
Artola-Igarza, JL:
Hosp Galdakao, Galdakao, Spain
Pacheco, MLA:
Hosp La Paz, Madrid, Spain
Markixana, IA:
Hosp Univ Cruces, Baracaldo, Spain
Fernandez, RS:
Hosp Gregorio Maranon, Madrid, Spain
Rubio, AA:
Hosp Manises, Valencia, Spain
Vazquez-Veiga, H:
Complexo Hosp Univ Santiago, Santiago de Compostela, Spain
Florez-Menendez, A:
Complejo Univ Hosp Pontevedra, Pontevedra, Spain
Dobao, PD:
Hosp Infanta Leonor, Madrid, Spain
Botella-Estrada, R:
Hosp Univ La Fe, Valencia, Spain
Garcia-Bracamonte, B:
Hosp Univ Doce Octubre, Madrid, Spain
Carnero-Gonzalez, L:
Hosp Univ Araba, Vitoria, Spain
Ruiz-Salas, V:
Hosp Santa Creu & Sant Pau, Barcelona, Spain
Sanchez-Sambucety, P:
Complejo Asistencial Univ Leon, Leon, Spain
Lopez-Estebaranz, JL:
Hosp Univ Fdn Alcorcon, Madrid, Spain
Gil, P:
Clin Univ Navarra, Pamplona, Spain
Barchino, L:
Hosp La Zarzuela, Madrid, Spain
Arenal, MM:
Hosp La Paz, Madrid, Spain
Ocerin-Guerra, I:
Hosp Univ Cruces, Baracaldo, Spain
Hueso, L:
Hosp Manises, Valencia, Spain
Seoane-Pose, MJ:
Complexo Hosp Univ Santiago, Santiago de Compostela, Spain
Gonzalez-Sixto, B:
Complejo Univ Hosp Pontevedra, Pontevedra, Spain
Cano-Martinez, N:
Hosp La Zarzuela, Madrid, Spain
Hosp Infanta Leonor, Madrid, Spain
Escutia-Munoz, B:
Hosp Univ La Fe, Valencia, Spain
Ortiz-Romero, PL:
Hosp Univ Doce Octubre, Madrid, Spain
Garcia-Doval, I:
Complexo Hosp Univ Vigo, Vigo, Spain
Acad Espanola Dermatol, Fdn Piel Sana, Madrid, Spain
Descalzo, MA:
Acad Espanola Dermatol, Fdn Piel Sana, Madrid, Spain
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